Lesson 284: PreAnesthetic Assessment of the Patient With Cornelia de Lange Syndrome

Course Authors:

Veronica Washington, MD, MPH, Intern, Louisiana State University School of Medicine, New Orleans, Louisiana

Alan D. Kaye, MD, PhD, DABPMb, Professor and chairman, Department of Anesthesiology, Louisiana State University School of Medicine, New Orleans, Louisiana

Registration Fee: $15.00
2.0 AMA PRA Category 1 CreditsTM
available until February 28, 2011

Reviewed By:

Elizabeth A.M. Frost, MD, Professor of anesthesiology, Mount Sinai School of Medicine, New York, New York

Review Date: October, 2009 

REGISTRATION INFORMATION:

Participants who do not possess a copy of Anesthesiology News can download and print the course material in an easy to read convenient  format.  Participants must reflect on the information presented, and then register to complete the exam and course evaluation online before the availability date listed above.  (CME credit is not valid past this date).  

Click on the link below to download and print the course material and post-test exam.  Register for the exam to enter your responses to receive CME credit.  There are ten questions in the examination and you must achieve a score of 80% or better to earn CME credit.  Following successful completion, your certificate will be immediately available online.  In addition, a historical record of  completed CME courses is maintained online in an individualized profile.  This includes copies of course certificates which can be printed at any time.

The registration fee for this course is $15.00

Physicians are provided with two opportunities to successfully complete the exam presented here. 

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CLICK HERE TO VIEW / PRINT COURSE MATERIAL

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NEEDS STATEMENT

Committee opinion and audience surveys have identified the need to present, from time to time, rarely encountered diseases for which there are anesthetic implications.

CASE HISTORY

A 9-month-old girl weighing 14 kg with longstanding gastroesophageal reflux disease was scheduled for surgery for Nissen fundoplication. She was diagnosed with CdLS, and recently had a cardiac evaluation that did not reveal any abnormalities. All laboratory test results were within normal limits.

LEARNING OBJECTIVES

At the end of this activity, the participant should be able to:

  1. Recognize and describe the clinical features of Cornelia de Lange syndrome (CdLS).

  2. List the major causes of mortality in patients with CdLS.

  3. Discuss the treatment of CdLS.

  4. Outline the current theory of CdLS pathogenesis.

  5. Explain the importance of a preoperative evaluation of these patients.

  6. Identify appropriate treatment of cardiac anomalies.

  7. Describe appropriate anesthetic management of hypoxia and hypercapnia.

  8. Discuss difficulties in managing the airway of the patient with CdLS.

  9. List anesthetics that are contraindicated for the patient with CdLS.

  10. Identify drugs recommended for inducing anesthesia in the patient with CdLS.

TARGET AUDIENCE:  Anesthesiologists

Accreditation Statement

Mount Sinai School of Medicine is accredited by the Accreditation Council for Continuing Medical Education (ACCME) to provide continuing medical education for physicians.

Credit Designation: The Mount Sinai School of Medicine designates each educational activity for a maximum of 2 AMA PRA Category 1 CreditsTM. Physicians should only claim credit commensurate with the extent of their participation in the activity.

It is the policy of Mount Sinai School of Medicine to ensure objectivity, balance, independence, and scientific rigor in all CME-sponsored educational activities. All faculty participating in the planning or implementation of a sponsored activity are expected to disclose to the audience any relevant financial relationships and to assist in resolving any conflict of interest that may arise from the relationship. Presenters must also make a meaningful disclosure to the audience of their discussions of unlabeled or unapproved drugs or devices.

Disclosures

Dr. Kaye has disclosed that he is a member of the speakers’ bureau of Baxter. The other author, reviewer, and editor have no relationships with pharmaceuti-cal companies or manufacturers of products to disclose. This educational activity may contain discussion of published and/or investigational uses of agents for the treatment of disease. Some uses of these agents have not been approved by the FDA. Please refer to the official prescribing information for each product for approved indications, contraindications, and warnings.

CONTACT INFORMATION

Questions regarding course content may be directed to Dr. Elizabeth Frost: ElzFrost@aol.com.

If you require technical assistance with completing this course, please contact Continuing Education Online Customer Service at 718-648-8080 or send e-mail to ceo.contact7@proceo.com.

CALL FOR WRITERS

If you would like to write a CME lesson in Anesthesiology News, please send an e-mail to Elizabeth A.M. Frost, MD, at ElzFrost@aol.com